Sfoglia per Autore
Sarcoplasmic reticulum-mitochondrial symbiosis: bidirectional signaling in skeletal muscle
2009-01-01 Rossi, Ae; Boncompagni, Simona; Dirksen, Rt
Fine-tuning of POPC liposomal leakage by the use of β-cyclodextrin and several hydrophobic guests
2010-01-01 Gasbarri, Carla; Guernelli, S.; Boncompagni, Simona; Angelini, Guido; Siani, Gabriella; DE MARIA, Paolo; Fontana, Antonella
The I4895T mutation in the type 1 ryanodine receptor induces fiber-type specific alterations in skeletal muscle that mimic premature aging.
2010-01-01 Boncompagni, Simona; Loy, Re; Dirksen, Rt; Franzini Armstrong, C.
Home-based functional electrical stimulation rescues permanently denervated muscles in paraplegic patients with complete lower motor neuron lesion.
2010-01-01 Kern, Helmut; Carraro, Ugo; Adami, Nicoletta; Biral, Donatella; Hofer, Christian; Forstner, Claudia; Mödlin, Michaela; Vogelauer, Michael; Pond, Amber; Boncompagni, Simona; Paolini, Cecilia; Mayr, Winfried; Protasi, Feliciano; Zampieri, Sandra
The evolution of the mitochondria-to-calcium release units relationship in vertebrate skeletal muscles.
2011-01-01 Franzini Armstrong, C; Boncompagni, Simona
Differential impact of mitochondrial positioning on mitochondrial Ca2+ uptake and Ca2+ spark suppression in skeletal muscle.
2011-01-01 Rossi Ann, E.; Boncompagni, Simona; Wei, Lan; Protasi, Feliciano; Dirksen Robert, T.
Mitochondrial superoxide flashes: metabolic biomarkers of skeletal muscle activity and disease
2011-01-01 Wei, Lan; Salahura, Gheorghe; Boncompagni, Simona; Kasischke Karl, A.; Protasi, Feliciano; Sheu Shey, Shing; Dirksen Robert, T.
THE NEURONAL GROWTH ASSOCIATED PROTEIN 43 IS EXPRESSED IN SKELETAL MUSCLE FIBERS CLOSE TO MITOCHONDRIA AND CALCIUM RELEASE UNITS.
2012-01-01 Guarnieri, Simone; Caprara, GIUSY ANNAMARIA; Morabito, Caterina; Boncompagni, Simona; Paolini, Cecilia; G., Fanò; Mariggio', Maria Addolorata
Triadin/Junctin double null mouse reveals a differential role for Triadin and Junctin in anchoring CASQ to the jSR and regulating Ca(2+) homeostasis
2012-01-01 Boncompagni, Simona; Thomas, M; Lopez, Jr; Allen, Pd; Yuan, Q; Kranias, Eg; Franzini Armstrong, C; Perez, C. F.
Sequential stages in the gradual formation and accumulation of tubular aggregates in aging fast twitch muscle: SERCA and Calsequestrin involvement.
2012-01-01 Boncompagni, Simona; Protasi, Feliciano; Franzini Armstrong, Clara
Mitochondrial dysfunction in skeletal muscle of amyloid precursor protein-overexpressing mice
2012-01-01 Boncompagni, Simona; Moussa Charbel, E. H.; Levy, Ezra; Pezone Matthew, J; Lopez Jose, R; Protasi, Feliciano; Shtifman, Alexander
Mice expressing T4826I-RYR1 are viable but exhibit sex- andgenotype-dependent susceptibility to malignant hyperthermia and muscle damage.
2012-01-01 Yuen, B; Boncompagni, Simona; Feng, W; Yang, T; Lopez, Jr; Matthaei, Ki; Goth, Sr; Protasi, Feliciano; Franzini Armstrong, C; Allen, Pd; Pessah, I. N.
Viral gene transfer rescues arrhythmogenic phenotype and ultrastructural abnormalities in adult calsequestrin-null mice with inherited arrhythmias.
2012-01-01 Denegri, M; Avelino Cruz, Je; Boncompagni, Simona; De Simone, Sa; Auricchio, A; Villani, L; Volpe, P; Protasi, Feliciano; Napolitano, C; Priori, Sg
Gold nanoparticles as scaffolds for new antiparkinson prodrugs
2013-01-01 DI CRESCENZO, Antonello; Sozio, Piera; Boncompagni, Simona; Marinelli, Lisa; Ippolito, Marina; DI STEFANO, Antonio; Fontana, Antonella
Orai1-dependent calcium entry promotes skeletal muscle growth and limits fatigue
2013-01-01 Lan Wei, Lapierre; Ellie M., Carrell; Boncompagni, Simona; Protasi, Feliciano; Robert T., Dirksen
Abnormal Propagation of Calcium Waves and Ultrastructural Remodeling in Recessive Catecholaminergic Polymorphic Ventricular Tachycardia.
2013-01-01 Liu, N; Denegri, M; Dun, W; Boncompagni, Simona; Lodola, F; Protasi, Feliciano; Napolitano, C; Boyden, P; Priori, Sg
Growth associated protein 43 is expressed in skeletal muscle fibers and is localized in proximity of mitochondria and calcium release units.
2013-01-01 Guarnieri, Simone; Morabito, Caterina; Paolini, Cecilia; Boncompagni, Simona; Pilla, R; FANO' ILLIC', Giorgio; Mariggio', Maria Addolorata
Post-natal heart adaptation in a knock-in mouse model of calsequestrin 2-linked recessive catecholaminergic polymorphic ventricular tachycardia
2014-01-01 Giorgia, Valle; Boncompagni, Simona; Roberta, Sacchetto; Protasi, Feliciano; Pompeo, Volpe
Single Delivery of an Adeno-Associated Viral Construct to Transfer the CASQ2 Gene to Knock-In Mice Affected by Catecholaminergic Polymorphic Ventricular Tachycardia Is Able to Cure the Disease From Birth to Advanced Age
2014-01-01 Denegri, M.; Bongianino, R.; Lodola, F.; Boncompagni, Simona; De Giusti, V. C.; Avelino Cruz, J. E.; Liu, N.; Persampieri, S.; Curcio, A.; Esposito, F.; Pietrangelo, L.; Marty, I.; Villani, L.; Moyaho, A.; Baiardi, P.; Auricchio, A.; Protasi, Feliciano; Napolitano, C.; Priori, S. G.
Age-dependent uncoupling of mitochondria from Ca2+ release units in skeletal muscle
2015-01-01 Pietrangelo, Laura; D'Incecco, Alessandra; Ainbinder, Alina; Michelucci, Antonio; Kern, Helmut; Dirksen, Robert T.; Boncompagni, Simona; Protasi, Feliciano
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Sarcoplasmic reticulum-mitochondrial symbiosis: bidirectional signaling in skeletal muscle | 2009 | Rossi, Ae; Boncompagni, Simona; Dirksen, Rt | |
Fine-tuning of POPC liposomal leakage by the use of β-cyclodextrin and several hydrophobic guests | 2010 | Gasbarri, Carla; Guernelli, S.; Boncompagni, Simona; Angelini, Guido; Siani, Gabriella; DE MARIA, Paolo; Fontana, Antonella | |
The I4895T mutation in the type 1 ryanodine receptor induces fiber-type specific alterations in skeletal muscle that mimic premature aging. | 2010 | Boncompagni, Simona; Loy, Re; Dirksen, Rt; Franzini Armstrong, C. | |
Home-based functional electrical stimulation rescues permanently denervated muscles in paraplegic patients with complete lower motor neuron lesion. | 2010 | Kern, Helmut; Carraro, Ugo; Adami, Nicoletta; Biral, Donatella; Hofer, Christian; Forstner, Claudia; Mödlin, Michaela; Vogelauer, Michael; Pond, Amber; Boncompagni, Simona; Paolini, Cecilia; Mayr, Winfried; Protasi, Feliciano; Zampieri, Sandra | |
The evolution of the mitochondria-to-calcium release units relationship in vertebrate skeletal muscles. | 2011 | Franzini Armstrong, C; Boncompagni, Simona | |
Differential impact of mitochondrial positioning on mitochondrial Ca2+ uptake and Ca2+ spark suppression in skeletal muscle. | 2011 | Rossi Ann, E.; Boncompagni, Simona; Wei, Lan; Protasi, Feliciano; Dirksen Robert, T. | |
Mitochondrial superoxide flashes: metabolic biomarkers of skeletal muscle activity and disease | 2011 | Wei, Lan; Salahura, Gheorghe; Boncompagni, Simona; Kasischke Karl, A.; Protasi, Feliciano; Sheu Shey, Shing; Dirksen Robert, T. | |
THE NEURONAL GROWTH ASSOCIATED PROTEIN 43 IS EXPRESSED IN SKELETAL MUSCLE FIBERS CLOSE TO MITOCHONDRIA AND CALCIUM RELEASE UNITS. | 2012 | Guarnieri, Simone; Caprara, GIUSY ANNAMARIA; Morabito, Caterina; Boncompagni, Simona; Paolini, Cecilia; G., Fanò; Mariggio', Maria Addolorata | |
Triadin/Junctin double null mouse reveals a differential role for Triadin and Junctin in anchoring CASQ to the jSR and regulating Ca(2+) homeostasis | 2012 | Boncompagni, Simona; Thomas, M; Lopez, Jr; Allen, Pd; Yuan, Q; Kranias, Eg; Franzini Armstrong, C; Perez, C. F. | |
Sequential stages in the gradual formation and accumulation of tubular aggregates in aging fast twitch muscle: SERCA and Calsequestrin involvement. | 2012 | Boncompagni, Simona; Protasi, Feliciano; Franzini Armstrong, Clara | |
Mitochondrial dysfunction in skeletal muscle of amyloid precursor protein-overexpressing mice | 2012 | Boncompagni, Simona; Moussa Charbel, E. H.; Levy, Ezra; Pezone Matthew, J; Lopez Jose, R; Protasi, Feliciano; Shtifman, Alexander | |
Mice expressing T4826I-RYR1 are viable but exhibit sex- andgenotype-dependent susceptibility to malignant hyperthermia and muscle damage. | 2012 | Yuen, B; Boncompagni, Simona; Feng, W; Yang, T; Lopez, Jr; Matthaei, Ki; Goth, Sr; Protasi, Feliciano; Franzini Armstrong, C; Allen, Pd; Pessah, I. N. | |
Viral gene transfer rescues arrhythmogenic phenotype and ultrastructural abnormalities in adult calsequestrin-null mice with inherited arrhythmias. | 2012 | Denegri, M; Avelino Cruz, Je; Boncompagni, Simona; De Simone, Sa; Auricchio, A; Villani, L; Volpe, P; Protasi, Feliciano; Napolitano, C; Priori, Sg | |
Gold nanoparticles as scaffolds for new antiparkinson prodrugs | 2013 | DI CRESCENZO, Antonello; Sozio, Piera; Boncompagni, Simona; Marinelli, Lisa; Ippolito, Marina; DI STEFANO, Antonio; Fontana, Antonella | |
Orai1-dependent calcium entry promotes skeletal muscle growth and limits fatigue | 2013 | Lan Wei, Lapierre; Ellie M., Carrell; Boncompagni, Simona; Protasi, Feliciano; Robert T., Dirksen | |
Abnormal Propagation of Calcium Waves and Ultrastructural Remodeling in Recessive Catecholaminergic Polymorphic Ventricular Tachycardia. | 2013 | Liu, N; Denegri, M; Dun, W; Boncompagni, Simona; Lodola, F; Protasi, Feliciano; Napolitano, C; Boyden, P; Priori, Sg | |
Growth associated protein 43 is expressed in skeletal muscle fibers and is localized in proximity of mitochondria and calcium release units. | 2013 | Guarnieri, Simone; Morabito, Caterina; Paolini, Cecilia; Boncompagni, Simona; Pilla, R; FANO' ILLIC', Giorgio; Mariggio', Maria Addolorata | |
Post-natal heart adaptation in a knock-in mouse model of calsequestrin 2-linked recessive catecholaminergic polymorphic ventricular tachycardia | 2014 | Giorgia, Valle; Boncompagni, Simona; Roberta, Sacchetto; Protasi, Feliciano; Pompeo, Volpe | |
Single Delivery of an Adeno-Associated Viral Construct to Transfer the CASQ2 Gene to Knock-In Mice Affected by Catecholaminergic Polymorphic Ventricular Tachycardia Is Able to Cure the Disease From Birth to Advanced Age | 2014 | Denegri, M.; Bongianino, R.; Lodola, F.; Boncompagni, Simona; De Giusti, V. C.; Avelino Cruz, J. E.; Liu, N.; Persampieri, S.; Curcio, A.; Esposito, F.; Pietrangelo, L.; Marty, I.; Villani, L.; Moyaho, A.; Baiardi, P.; Auricchio, A.; Protasi, Feliciano; Napolitano, C.; Priori, S. G. | |
Age-dependent uncoupling of mitochondria from Ca2+ release units in skeletal muscle | 2015 | Pietrangelo, Laura; D'Incecco, Alessandra; Ainbinder, Alina; Michelucci, Antonio; Kern, Helmut; Dirksen, Robert T.; Boncompagni, Simona; Protasi, Feliciano |
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