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Unexpected structural and functional consequences of the R33Q homozygous mutation in cardiac calsequestrin. A complex arrhythmogenic cascade in a knock-in mouse model. 2008 Rizzi, N; Nian, L; Napolitano, C; Nori, A; Turcato, F; Colombi, B; Bicciato, S; Arcelli, D; Spedito, A; Scelsi, M; Villanil, ; Esposito, G; Boncompagni, Simona; Protasi, Feliciano; Volpe, P; Priori, Sg
A sub-population of rat muscle fibers maintains an assessable excitation-contraction coupling mechanism after long-standing denervation, despite lost contractility 2009 Squecco, R; Carraro, U; Kern, H; Pond, A; Adami, N; Biral, D; Vindigni, V; Boncompagni, S; Pietrangelo, T; Bosco, G; Fanò, G; Marini, M; Abruzzo, Pm; Germinario, E; Danieli-Betto, D; Protasi, F; Francini, F; Zampieri, S
Anesthetic- and heat-induced sudden death in calsequestrin-1 knockout mice. 2009 Dainese, Marco; Quarta, M; Lyfenko, Ad; Paolini, Cecilia; Canato, M; Dirksen, Rt; Reggiani, C; Protasi, Feliciano
Characterization and temporal development of cores in a mouse model of malignant hyperthermia. 2009 Boncompagni, Simona; Rossi, Ae; Micaroni, M; Hamilton, Sl; Dirksen, Rt; Franzini Armstrong, C; Protasi, Feliciano
Calsequestrin-1: a new candidate gene for malignant hyperthermia (MH) and environmental heat stroke (EHS) 2009 Protasi, Feliciano; Paolini, Cecilia; Dainese, Marco
Mitochondria are linked to calcium stores in striated muscle by developmentally regulated tethering structures 2009 Boncompagni, Simona; Rossi, Ae; Micaroni, M; Beznoussenko, Gv; Polishchuk, Rs; Dirksen, Rt; Protasi, Feliciano
Paradoxical buffering of calcium by calsequestrin demonstrated for the calcium store of skeletal muscle. 2010 Royer, Leandro; Sztretye, Monika; Manno, Carlo; Pouvreau, Sandrine; Zhou, Jingsong; Knollmann Bjorn, C.; Protasi, Feliciano; Allen Paul, D.; Ríos, Eduardo
Home-based functional electrical stimulation rescues permanently denervated muscles in paraplegic patients with complete lower motor neuron lesion. 2010 Kern, Helmut; Carraro, Ugo; Adami, Nicoletta; Biral, Donatella; Hofer, Christian; Forstner, Claudia; Mödlin, Michaela; Vogelauer, Michael; Pond, Amber; Boncompagni, Simona; Paolini, Cecilia; Mayr, Winfried; Protasi, Feliciano; Zampieri, Sandra
Massive alterations of sarcoplasmic reticulum free calcium in skeletal muscle fibers lacking calsequestrin revealed by a genetically encoded probe. 2010 Canato, Marta; Scorzeto, Michele; Giacomello, Margherita; Protasi, Feliciano; Reggiani, Carlo; Stienen Ger, J. M.
Mitochondrial superoxide flashes: metabolic biomarkers of skeletal muscle activity and disease 2011 Wei, Lan; Salahura, Gheorghe; Boncompagni, Simona; Kasischke Karl, A.; Protasi, Feliciano; Sheu Shey, Shing; Dirksen Robert, T.
Lessons from calsequestrin-1 ablation in vivo: much more than a Ca2+ buffer after all. 2011 Protasi, Feliciano; Paolini, Cecilia; Canato, Marta; Reggiani, Carlo; Quarta, Marco
Differential impact of mitochondrial positioning on mitochondrial Ca2+ uptake and Ca2+ spark suppression in skeletal muscle. 2011 Rossi Ann, E.; Boncompagni, Simona; Wei, Lan; Protasi, Feliciano; Dirksen Robert, T.
Differential effect of calsequestrin ablation on structure and function of fast and slow twitch skeletal fibers. 2011 Paolini, Cecilia; Quarta, Marco; D’Onofrio, Laura; Reggiani, Laura; Protasi, Feliciano
Atrophy/hypertrophy cell signaling in muscles of young athletes trained with vibrational-proprioceptive stimulation. 2011 Kern, Helmut; Pelosi, Laura; Coletto, Luisa; Musarò, Antonio; Sandri, Marco; Vogelauer, Michael; Trimmel, Lukas; Cvecka, Jan; Hamar, Dusan; Kovarik, Josef; Löfler, Stefan; Sarabon, Nejc; Protasi, Feliciano; Adami, Nicoletta; Biral, Donatella; Zampieri, Sandra; Carraro, Ugo
Potential Antibacterial Activity of Carvacrol-Loaded PLGA Nanoparticles against Microbial Biofilm 2011 Iannitelli, Antonio; Grande, Rossella; DI STEFANO, Antonio; DI GIULIO, Mara; Sozio, Piera; DA SILVA BESSA, LUCINDA JANETE; Laserra, Sara; Paolini, Cecilia; Protasi, Feliciano; Cellini, Luigina
Mice expressing T4826I-RYR1 are viable but exhibit sex- andgenotype-dependent susceptibility to malignant hyperthermia and muscle damage. 2012 Yuen, B; Boncompagni, Simona; Feng, W; Yang, T; Lopez, Jr; Matthaei, Ki; Goth, Sr; Protasi, Feliciano; Franzini Armstrong, C; Allen, Pd; Pessah, I. N.
Knowledge and Health Care resource allocation: CME/CPD course guidelines-based efficacy 2012 Braido, Fulvio; Comaschi, M.; Valle, I.; Delgado, L.; Coccini, A.; Guerrera, P.; Stagi, E.; Canonica, G. W.; Angino, A.; Baldacci, S.; Borbotti, M.; Cerrai, S.; Di Pede, F.; Maio, S.; Mangione, M.; Martini, F.; Pala, A. P.; Piegaia, B.; Sarno, G.; Silvi, P.; Viegi, G.; Dente, F.; Bacci, E.; Paggiaro, P.; Bancalari, L.; Foschino, M. P.; Moscato, G.; Pilucchi, A.; Bresciani, M.; Pierimarchi, P.; Brunetto, B.; Iacovacci, P.; Pini, C.; Tinghino, R.; Forestiere, F.; Perucci, C. A.; Porta, D.; Ancona, L.; Protasi, Feliciano; Lazazzera, B.; Ziroli, V.; D'Armini, E.; Campanile, S. Festa; Ferri, M.; Lorusso, P.; Pistelli, R.; Salotti, R.; Santagati, M.; Agea, E.; Casciari, C.; Murgia, N.; Spinozzi, F.; Bonifazi, Ancona F.; Antonicelli, L.; Braschi, M. C.; Conti, V.; Filippelli, A.; Corbi, G. M.; Russomanno, G.; Baiardini, I.; Balbi, F.; Ferraioli, G.; Bordo, A.; Cerveri, I.; Corsico, A.; Grosso, A.
Viral gene transfer rescues arrhythmogenic phenotype and ultrastructural abnormalities in adult calsequestrin-null mice with inherited arrhythmias. 2012 Denegri, M; Avelino Cruz, Je; Boncompagni, Simona; De Simone, Sa; Auricchio, A; Villani, L; Volpe, P; Protasi, Feliciano; Napolitano, C; Priori, Sg
Sequential stages in the gradual formation and accumulation of tubular aggregates in aging fast twitch muscle: SERCA and Calsequestrin involvement. 2012 Boncompagni, Simona; Protasi, Feliciano; Franzini Armstrong, Clara
Mitochondrial dysfunction in skeletal muscle of amyloid precursor protein-overexpressing mice 2012 Boncompagni, Simona; Moussa Charbel, E. H.; Levy, Ezra; Pezone Matthew, J; Lopez Jose, R; Protasi, Feliciano; Shtifman, Alexander
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