BONCOMPAGNI, SIMONA

BONCOMPAGNI, SIMONA  

DIPARTIMENTO DI NEUROSCIENZE, IMAGING E SCIENZE CLINICHE  

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A sub-population of rat muscle fibers maintains an assessable excitation-contraction coupling mechanism after long-standing denervation, despite lost contractility 2009 Squecco, R; Carraro, U; Kern, H; Pond, A; Adami, N; Biral, D; Vindigni, V; Boncompagni, S; Pietrangelo, T; Bosco, G; Fanò, G; Marini, M; Abruzzo, Pm; Germinario, E; Danieli-Betto, D; Protasi, F; Francini, F; Zampieri, S
Ablation of palladin in adult heart causes dilated cardiomyopathy associated with intercalated disc abnormalities 2023 Mastrototaro, Giuseppina; Carullo, Pierluigi; Zhang, Jianlin; Scellini, Beatrice; Piroddi, Nicoletta; Nemska, Simona; Filomena, Maria Carmela; Serio, Simone; Otey, Carol A; Tesi, Chiara; Emrich, Fabian; Linke, Wolfgang A; Poggesi, Corrado; Boncompagni, Simona; Bang, Marie-Louise
Abnormal Propagation of Calcium Waves and Ultrastructural Remodeling in Recessive Catecholaminergic Polymorphic Ventricular Tachycardia. 2013 Liu, N; Denegri, M; Dun, W; Boncompagni, Simona; Lodola, F; Protasi, Feliciano; Napolitano, C; Boyden, P; Priori, Sg
Addendum: Exercise-dependent formation of new junctions that promote STIM1-Orai1 assembly in skeletal muscle 2018 Boncompagni, S.; Michelucci, A.; Pietrangelo, L.; Dirksen, R. T.; Protasi, F.
Aerobic Training Prevents Heatstrokes in Calsequestrin-1 Knockout Mice by Reducing Oxidative Stress 2018 Guarnier, Flávia Alessandra; Michelucci, Antonio; Serano, Matteo; Pietrangelo, Laura; Pecorai, Claudia; Boncompagni, Simona; Protasi, Feliciano
Age-dependent oxidative stress and functional capacity of human skeletal muscle satellite cells 2003 Pietrangelo, Tiziana; DI DONNA, Silvia; Puglielli, Cristina; Boncompagni, Simona; DI TANO, Guglielmo; FANO' ILLIC', Giorgio; Fulle, Stefania
Age-dependent uncoupling of mitochondria from Ca2+ release units in skeletal muscle 2015 Pietrangelo, Laura; D'Incecco, Alessandra; Ainbinder, Alina; Michelucci, Antonio; Kern, Helmut; Dirksen, Robert T.; Boncompagni, Simona; Protasi, Feliciano
Ageing Causes Ultrastructural Modification to Calcium Release Units and Mitochondria in Cardiomyocytes 2021 Di Fonso, A.; Pietrangelo, L.; D'Onofrio, L.; Michelucci, A.; Boncompagni, S.; Protasi, F.
Allele-Specific Silencing of Mutant mRNA Rescues Ultrastructural and Arrhythmic Phenotype in Mice Carriers of the R4496C Mutation in the Ryanodine Receptor Gene ( RYR2) 2017 Bongianino, Rossana; Denegri, Marco; Mazzanti, Andrea; Lodola, Francesco; Vollero, Alessandra; Boncompagni, Simona; Fasciano, Silvia; Rizzo, Giulia; Mangione, Damiano; Barbaro, Serena; DI FONSO, Alessia; Napolitano, Carlo; Auricchio, Alberto; Protasi, Feliciano; Priori, Silvia G.
An Ryr1I4895T mutation abolishes Ca2+ release channel function and delays development in homozygous offspring of a mutant mouse line. 2007 Zvaritch, Elena; Depreux, Frederic; Kraeva, Natasha; E Loy, Ryan; A Goonasekera, Sanjeewa; Boncompagni, Simona; Kraev, Alexander; O Gramolini, Anthony; T Dirksen, Robert; Franzini-Armstrong, Clara; E Seidman, Christine; G Seidman, J; H Maclennan, David
Antioxidant Treatment Reduces Formation of Structural Cores and Improves Muscle Function in RYR1 Y522S/WT Mice 2017 Michelucci, Antonio; De Marco, Alessandro; Guarnier, Flavia A.; Protasi, Feliciano; Boncompagni, Simona
Atrophy, but not necrosis, in rabbit skeletal muscle denervated for periods up to one year. 2007 Ashley, Z; Sutherland, H; Lanmuller, H; Russold, M. F.; Unger, E; Bijak, M; Mayr, W; Boncompagni, Simona; Protasi, Feliciano; Salmons, S; AND JARVIS, J. C.
Atrophy-resistant fibers in permanent peripheral denervation of human skeletal muscle. 2008 Biral, D; Kern, H; Adami, N; Boncompagni, Simona; Protasi, Feliciano; Carraro, U.
Calcium entry units (CEUs): perspectives in skeletal muscle function and disease 2020 Protasi, Feliciano; Pietrangelo, Laura; Boncompagni, Simona
Characterization and temporal development of cores in a mouse model of malignant hyperthermia. 2009 Boncompagni, Simona; Rossi, Ae; Micaroni, M; Hamilton, Sl; Dirksen, Rt; Franzini Armstrong, C; Protasi, Feliciano
Constitutive assembly of Ca2+ entry units in soleus muscle from calsequestrin knockout mice 2022 Michelucci, A.; Pietrangelo, L.; Rastelli, G.; Protasi, F.; Dirksen, R. T.; Boncompagni, S.
Defective endoplasmic reticulum-mitochondria contacts and bioenergetics in SEPN1-related myopathy 2020 Filipe, Anne; Chernorudskiy, Alexander; Arbogast, Sandrine; Varone, Ersilia; Villar-Quiles, Rocío-Nur; Pozzer, Diego; Moulin, Maryline; Fumagalli, Stefano; Cabet, Eva; Dudhal, Swati; De Simoni, Maria-Grazia; Denis, Raphaël; Vadrot, Nathalie; Dill, Corinne; Giovarelli, Matteo; Szweda, Luke; De Palma, Clara; Pinton, Paolo; Giorgi, Carlotta; Viscomi, Carlo; Clementi, Emilio; Missiroli, Sonia; Boncompagni, Simona; Zito, Ester; Ferreiro, Ana
Deletion of the microtubule-associated protein 6 (MAP6) results in skeletal muscle dysfunction 2018 Sébastien, Muriel; Giannesini, Benoit; Aubin, Perrine; Brocard, Julie; Chivet, Mathilde; Pietrangelo, Laura; Boncompagni, Simona; Bosc, Christophe; Brocard, Jacques; Rendu, John; Gory-Fauré, Sylvie; Andrieux, Annie; Fourest-Lieuvin, Anne; Fauré, Julien; Marty, Isabelle
Diaphragm Fatigue in SMNΔ7 Mice and Its Molecular Determinants: An Underestimated Issue 2023 Cadile, F.; Recchia, D.; Ansaldo, M.; Rossi, P.; Rastelli, G.; Boncompagni, S.; Brocca, L.; Pellegrino, M. A.; Canepari, M.
Differential impact of mitochondrial positioning on mitochondrial Ca2+ uptake and Ca2+ spark suppression in skeletal muscle. 2011 Rossi Ann, E.; Boncompagni, Simona; Wei, Lan; Protasi, Feliciano; Dirksen Robert, T.